先天性红细胞生成障碍性贫血诊断现状

茹永新; 董树旭; 赵轼轩

doi:10.13201/j.issn.1004-2806.2014.01.024

先天性红细胞生成障碍性贫血诊断现状

- 中国医学科学院北京协和医学院血液病医院血液学研究所病理中心(天津, 300041)

详细信息

通讯作者: 茹永新,E-mail:ruyongxin1@foxmail.com

中图分类号: R556.5

收稿日期: 2012-12-10

Diagnostic status of congenital dyserythropoietic anemias

More Information

Corresponding author: RU Yongxin, E-mail: ruyongxin1@foxmail.com

Received Date: 10 December 2012

摘要

- 先天性红细胞生成障碍性贫血 /
- 发病率 /
- 实验室检查
Abstract: Congenital dyserythropoietic anemias (CDAs) is a rare familial hereditary anemia disease with manifestations of chronic anemia,jaundice,abnormal erythroid cell morphology and hemolysis.CDAs may be complicated with hemochromatosis at the terminal stage and could occur hepatosplenomegaly.The disease is mainly reported in foreign and rarely reported in China.In this paper,we summarized and analyzed the incidence and diagnostic differences of CDAs in domestic and international research.
- congenital dyserythropoietic anemias /
- incidence /
- laboratory examination

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参考文献(21)

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