Primary biliary cirrhosis secondary to myelofibrosis:a case report and literature review
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Abstract: A case of primary biliary cirrhosis (PBC) initially presented with myelofibrosis (MF) was reported.Combined with clinical data and literature review,we analyzed the causes of missed diagnosis of PBC.Hematologists need to rule out autoimmune diseases in patients with abnormal blood counts.Early symptoms of PBC are not typical,and patients accompanying with cholestasis should be detected the related antibody.
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Key words:
- primary biliary cirrhosis /
- myelofibrosis
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[1] 陈灝珠, 林果为.实用内科学[M].13版.北京:人民卫生出版社, 2013:2090-2093.
[2] 徐东, 张奉春.原发性胆汁性肝硬化与抗gp210抗sp100抗体相关性的研究[J].中华风湿病学杂志, 2008, 12 (8):540-542.
[3] Lindor KD, Gershwin ME, Poupon R.Primary biliary cirrhosis[J].Hepatology, 2009, 50:291-308.
[4] 陈竺, 陈赛娟, 主译.威廉姆斯血液学[M].8版.北京:人民卫生出版社, 2011:1283-1300.
[5] 黄艳, 孙嘉峰.继发性与原发性骨髓纤维化骨髓组织形态学观察及临床意义[J].山西医科大学学报, 2012, 43 (6):453-456.
[6] 董家蔷, 张剑.80例继发性骨髓纤维化患者临床特点和骨髓活检分析[J].哈尔滨医科大学学报, 2009, 43 (6):603-605, 608.
[7] Hernández-Boluda JC, Jiménez M.Idiopathic myelofibrosis associated with primary biliary cirrhosis[J].Leuk Lymphoma, 2002, 43:673-674.
[8] Kornblihtt LI, Vassalllu PS.Primary myelofibrosis in apatient who developed primary biliary cirrhosis, autoimmune hemolytic anemia and fibrillary glomerulonephritis[J].Ann Hematol, 2008, 87:1019-1020.
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